Tinnitus

   Incidence 10-20% of population

   Pulsatile vs non-pulsatile

Aetiology

 

Non-pulsatile

   Hearing loss (Most common by far)

Pulsatile

Common causes

   Unknown                                      23%

   Arterial stenoses                          18%

   Intracranial hypertension               16%

   Venous anatomical variant            12%

   Other                                           8%

   Dural AVF                                    7%

   Vessel rich tumour (AV connection) 6%

   Arterial anatomical variants           4%

   Capillary hyperaemia                     3%

   Direct AVF                                   2%

   Aneurysm                                    1%

 

Full list

   Tumour

o   Paraganglioma (most common)

-   Glomus typanicum or glomus jugulare (auricular branch of nerve)

o   Meningioma

o   Endolymphatic sac tumour

o   Other skull base tumours

   Vascular – Arterial

o   Aberrant ICA

o   Persistence of stapedial artery

o   ICA dehiscence

o   Persistent trigeminal artery

o   Arterial stenosis or dissection

o   Dural AVF

o   Aneurysm (very rare)

o   Vascular loop in IAM (non a proven link)

   Vascular – venous

o   Transverse sinus stenosis

-   Intrinsic (Arachnoid granulation/thrombosis)

-   Extrinsic (IIH)

o   Sigmoid sinus wall anomalies (dehiscence or diverticulum) - ?very common cause 

-   Outpouching of sigmoid sinus into mastoid

o   Emissary vein enlargement

o   Jugular bulb abnormalities (most probably incidental)

-   High riding jugular bulb (above level of IAM)

-   Dehiscence

   Bone abnormalities/dysplasia

o   Otospongiosis

o   Paget;s

o   Facial nerve venous malformation

o   Superior semicircular canal dehiscence

 

Diagnosis

   Bruit on auscultation - ?arterial cause

   Cessation of tinnitus with compression of IJV – venous cause

 

Investigation

Imaging

   Depends on cause

   Low yield in standard tinnitus

   Higher yield if unilateral hearing loss or pulsatile

   Pulsatile:

o   MRA/MRV

o   CT skull base

References

Review article

Pulsatile Tinnitus

Imaging and Differential Diagnosis

Dtsch Arztebl Int 2013; 110(26): 451-8. DOI: 10.3238/arztebl.2013.0451

Hofmann, EBehr, RNeumann-Haefelin, TSchwager, K