Orbital disease

 

Orbital disease

•   Endocrine

o   Thyroid -associated ophthalmopathy

o   Acromegaly

•   Idiopathic orbital inflammatory syndrome

o   IgG4

o   Idopathic

•   Systemic inflammatory disease with orbital involvement:

o   Sarcoidosis

o   GCA

o   Wegener’s granulomatosis

o   Polyarteritis nodosa

o   SLE

o   Gout

o   Psoriatic arthritis

o   Rheumatoid arthritis

o   Bechet

o   IBD

o   Histiocytic disorders

-   Histiocytosis x

-   Erdheim-Chester disease

•   Infectious disease

o   Cellulitis

o   TB

o   Syphilis

o   Fungal – mucormycosis

o   Aspergillosis

o   Allergic fungal sinusitis

o   Mucocele

o   Silent sinus syndrome

•   Malignant

o   Lymphoma

o   Metastatic disease

o   Rhabdomyosarcoma

o   Lacrimal gland tumours

o   Neurogenic tumours

-   Glioma, meningioma, schwannoma

o   Vascular tumours

-   Cavernous haemangioma

-   Lymphangioma

-   Venous angioma (Varix)

-   Haemangioblastoma

-   Haemangiopericytoma

•   Other cystic lesions

o   Dermoids

•   Vascular

o   Carotid-cavernous fistula

o   Cavernous sinus thrombosis

•   Amyloidosis

·         Trauma

DDx – Enlarged extraocular muscles

 

•   Thyroid -associated ophthalmopathy

•   Acromegaly

•   Idiopathic orbital inflammatory syndrome

•   Lymphoma

•   Metastatic disease

•   Rhabdomyosarcoma

•   Sarcoidosis

•   Wegener’s granulomatosis

•   Amyloidosis

•   Trichinosis

 

Orbital Apex syndrome

 

Orbital apex syndrome

Superior orbital fissure syndrome

Cavernous sinus syndrome

Optic nerve

+

 

 

CN III

+

+

+

CN IV

+

+

+

CN VI

+

+

+

CNV – Div 1

+

+

+

CNV – Div 2

 

 

+

CNV – Div 3